Síndrome de Hipertensión Intracraneana como manifestación inhabitual del Síndrome de Sjögren. Caso Clínico

Autores/as

  • Dominga García Hospital Padre Hurtado Facultad de Medicina Clínica Alemana - Universidad del Desarrollo
  • Cristian Labarca Hospital Padre Hurtado Facultad de Medicina Clínica Alemana - Universidad del Desarrollo

Palabras clave:

Intracranial Hypertension, Pseudotumor Cerebri, Sjogren's Syndrome

Resumen

Neurological manifestations such as polyneuropathy are reported in 8-49% of cases with Sjögren’s Syndrome (SjS), but central nervous system involvement is seldom described. We report a 46-year-old woman with a history of SjS with distal renal tubular acidosis and autoimmune thyroiditis. She consulted in the emergency room for a five-days history of holocranial headache and explosive vomiting. Fundoscopy showed bilateral papilledema. Brain computed tomography (CT) without contrast showed diffuse encephalic edema, with effacement of sulci and restriction of peritruncal cisterns. Brain AngioCT ruled out thrombosis, and brain magnetic resonance (MRI) was without structural alterations or hydrocephalus. Lumbar puncture had increased cerebrospinal fluid output pressure but without cytochemical alterations, and negative gram, cultures and filmarray. The diagnosis of Intracranial Hypertension Syndrome (ICHTS) of probable autoimmune etiology in the context of SjS was proposed, and management with high-dose corticosteroids was initiated with favorable clinical and imaging response.

Biografía del autor/a

Dominga García, Hospital Padre Hurtado Facultad de Medicina Clínica Alemana - Universidad del Desarrollo

Residente de Medicina Interna Hospital Padre Hurtado Facultad de Medicina Clínica Alemana - Universidad del Desarrollo

Cristian Labarca, Hospital Padre Hurtado Facultad de Medicina Clínica Alemana - Universidad del Desarrollo

Reumatólogo Hospital Padre Hurtado Facultad de Medicina Clínica Alemana - Universidad del Desarrollo

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Publicado

2023-06-19

Cómo citar

García, D., & Labarca, C. (2023). Síndrome de Hipertensión Intracraneana como manifestación inhabitual del Síndrome de Sjögren. Caso Clínico. Revista Médica De Chile, 151(3). Recuperado a partir de https://www.revistamedicadechile.cl/index.php/rmedica/article/view/10284

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