Trasplante hepático por insuficiencia cardíaca secundaria a telangiectasia hemorrágica hereditaria (TJJ) o enfermedad de Rendu Osler Weber. Caso Clínico

Vanessa Ahumada, Rodrigo Tejos, Felipe Moraga, Pablo Achurra, Iván Godoy, Soledad Loyola, Javiera Torres, Marianne Kolbach, Carlos Benítez, Juan Francisco Guerra, Nicolás Jarufe, Jorge Martínez

Resumen


Liver involvement by multiple arterio-venous shunts in hereditary hemorrhagic telangiectasia can lead to severe heart failure. Total hepatectomy with liver transplantation has emerged as a therapeutic option for severe cases where other therapies have failed. We report a 51 years old male who underwent a liver transplant for this condition, with full cardiac recovery within the first year after receiving the allograft. Nine years after transplantation, he remains with normal functional capacity and normal liver function tests.

Palabras clave


Heart Failure; Liver Transplantation; Telangiectasia, Hereditary Hemorrhagic

Texto completo:

PDF final